ICD-10-CM Neuro-Ophthalmology

Disorders of the Nervous System

Type RT LT OU SINGLE CODE UNSPECIFIED

Amaurosis fugax 362.34 X X X G45.3 X

Horner’s Syndrome 337.9 X X X G90.2 X

Blepharospasm 333.81 X X X G24.5 X

Multiple sclerosis 340 X X X G35 X

Transient cerebral ischemic attack, unspecified (eg. TIA) 435.9 X X X G45.9 X

Benign intracranial hypertension 348.2 X X X G93.2 X

Ophthalmoplegic migraine, not intractable 346.2 X X X G43.B0 X

Ophthalmoplegic migraine, intractable 346.2 X X X G43.B1 X

Myasthenia gravis without (acute) exacerbation 358.00 X X X G70.00 X

Myasthenia gravis with (acute) exacerbation 358.01 X X X G70.01 X

Clonic hemifacial spasm 351.8 X X X G51.3 X

Disorders of Optic Nerve

Type RT LT OU SINGLE CODE UNSPECIFIED

Glaucomatous optic atrophy 377.14 H47.231 H47.232 H47.233 X H47.239

Optic papillitis 377.31 H46.01 H46.02 H46.03 X H46.00

Retrobulbar neuritis 377.32 H46.11 H46.12 H46.13 X H46.10

Unspecified optic atrophy 377.10 X X X H47.20 X

Primary optic atrophy 377.11 H47.211 H47.212 H47.213 X H47.219

Unspecified optic neuritis 377.30 X X X H46.9 X

Other optic neuritis 377.39 X X X H46.8 X

Pseudopapilledema of optic disc 377.24 H47.331 H47.332 H47.333 X H47.339

Unspecified papilledema 377.00 X X X H47.10 X

Ischemic optic neuropathy 377.41 H47.011 H47.012 H47.013 X H47.019

Disorders of optic chiasm 377.51 X X X H47.49 X

Disorders of optic chiasm associated with other neoplasms 377.52 X X X H47.42 X

Disorders of optic chiasm associated with vascular disorders 377.53 X X X H47.43 X

Disorders of optic chiasm associated with inflammatory disorders

X X X H47.41 X
377.54

1
Disorders of Optic Nerve (Continued)
Other disorders of optic nerve, NOC (eg.. compression of optic
H47.091 H47.092 H47.093 X H47.099
nerve) 377.49

Toxic optic neuropathy 377.34 X X X H46.3 X

Nutritional optic neuropathy 377.33 X X X H46.2 X

Hereditary optic atrophy 377.16 X X X H47.22 X

Cortical blindness 377.75 H47.611 H47.612 X X H47.619

Miscellaneous
Type RT LT OU SINGLE CODE UNSPECIFIED

Granuloma of orbit (eg. Pseudotumor (inflammatory) of orbit)

H05.111 H05.112 H05.113 X H05.119
376.11

Tonic pupil 379.46 H57.051 H57.052 H57.053 X H57.059

Benign neoplasm of pituitary gland 227.3 X X X D35.2 X

Benign neoplasm of unspecified site of orbit 224.1 D31.61 D31.62 X X D31.60

Anisocoria 379.41 X X X H57.02 X

Conversion disorder with sensory symptom or deficit 300.11 X X X F44.6 X

Benign neoplasm of cerebral meninges 225.2 X X X D32.0 X

Ocular pain 379.91 H57.11 H57.12 H57.13 X H57.10

Thyrotoxicosis with diffuse goiter with thyrotoxic crisis or storm

X X X E05.01 X
(eg. Graves’ Disease, Exophthalmic or toxic goiter NOS) 376.21
Thyrotoxicosis with diffuse goiter without thyrotoxic crisis or storm
X X X E05.00 X
(eg. Graves’ Disease, Exophthalmic or toxic goiter NOS) 376.21

Mydriasis 379.43 X X X H57.04 X

Anisocoria 379.41 X X X H57.02 X

Other specified disorders of binocular movement 378.85

X X X H51.8 X
(eg. Skew deviation) 378.87

Convergence insufficiency 378.83 X X X H51.11 X

Internuclear ophthalmoplegia 378.86 H51.21 H51.22 H51.23 X H51.20

Other giant cell arteritis 446.5 X X X M31.6 X

Tonic Pupil 379.46 H57.051 H57.052 H57.053 X H57.059

Other subjective visual disturbances (eg. Visual halos) 368.15 X X X H53.19 X

Elevated erythrocyte sedimentation rate 790.4 X X X R70.0 X

Cerebral infarction, unspecified (eg. Stroke) 434.1 X X X I63.9 X

Transient cerebral ischemic attack, unspecified (eg. TIA) 435.9 X X G45.9 X X

Malignant neoplasm of orbit 190.1 C69.61 C69.62 X X C69.60

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Miscellaneous (Continued)
Progressive external ophthalmoplegia 378.72 H49.41 H49.42 H49.43 X H49.40

Focal chorioretinal inflammation, juxtapapillary 363.05 H30.011 H30.012 H30.013 X H30.019

Acquired color vision deficiency 368.55 X X X H533.52 X

Scotoma of blind spot 368.42 H53.421 H53.422 H53.423 X H53.429

Partial retinal atery occlusion (eg. Hollenhorst’s plaque) 362.33 H34.211 H34.212 H34.213 X H34.219

Palsy (spasm) of conjugate gaze 378.81 X X X G51.0 X

Diplopia (Double vision) 368.2 X X X H53.2 X

Other Strabismus
Type RT LT OU SINGLE CODE UNSPECIFIED

Esophoria 378.41 X X X H50.51 X

Exophoria 378.42 X X X H50.52 X

Vertical strabismus (eg. Hypertropia) 378.81 H50.21 H50.22 X X X

Palsies
Type RT LT OU SINGLE CODE UNSPECIFIED

Third ocular motor nerve 378.51, 378.52 H49.01 H49.02 H49.03 X H49.00

Fourth ocular motor nerve 378.53 H49.11 H49.12 H49.13 X H49.10

Sixth ocular motor nerve 378.54 H49.21 H49.22 H49.23 X H49.20

Ptosis
Type RT LT OU SINGLE CODE UNSPECIFIED

Congenital 743.61 X X X Q10.0 X

Mechanical 374.33 H02.411 H02.412 H02.413 X H02.419

Myogenic 374.32 H02.421 H02.422 H02.423 X H02.429

Paralytic 374.31 H02.431 H02.432 H02.433 X H02.439

3
 Visual Field Disturbances
Type RT LT OU SINGLE CODE UNSPECIFIED

Unspecified visual field defects 368.40 X X X H53.40 X

Transient visual loss (eg. scintillating scotoma) 368.12 H53.121 H53.122 H53.123 X H53.129

Homonymous bilateral field defects 368.46 H53.461 H53.462 X X H53.469

Heteronymous bilateral field defects 368.47 X X X H53.47 X

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