Paediatric Cardiology: Post CSCST Training in
Paediatric Cardiology: Post CSCST Training in
Paediatric Cardiology: Post CSCST Training in
PAEDIATRIC CARDIOLOGY
Table of Contents
Introduction ............................................................................................................................................ 5
Recruitment and Selection.................................................................................................................. 5
Duration and Organisation of Training ............................................................................................... 5
Training Programme ........................................................................................................................... 5
Trainee Numbers ................................................................................................................................ 5
ePortfolio ............................................................................................................................................ 6
Programme Management ................................................................................................................... 6
Specialty Section ..................................................................................................................................... 7
Growth and Nutrition ......................................................................................................................... 8
Lifestyle ............................................................................................................................................... 9
Evaluation of a Child with a Cardiac Murmur ................................................................................... 10
Evaluation of the child with Chest Pain, Palpitations or Syncope .................................................... 11
Arrhythmias ...................................................................................................................................... 13
Cardiovascular Collapse in Infancy.................................................................................................... 15
Cardiac Failure in Infants and Children ............................................................................................. 16
Acyanotic Congenital Heart Disease throughout Childhood ............................................................ 17
Cyanotic Heart Disease in the Newborn Period................................................................................ 18
Cyanotic Heart Disease beyond the Newborn Period ...................................................................... 19
Practical Procedures and Investigations ........................................................................................... 21
Chest X-Ray ....................................................................................................................................... 22
Transthoracic Echocardiography ...................................................................................................... 23
Ambulatory ECG and External Cardiac Loop Recorder ..................................................................... 25
Ambulatory Blood Pressure .............................................................................................................. 26
Exercise Tests .................................................................................................................................... 27
ECG with Adenosine Challenge ......................................................................................................... 28
Tilt Table Testing ............................................................................................................................... 29
Cardiac Pacing ................................................................................................................................... 30
Cardiovascular evaluation of the child with features of a syndrome or genetic condition.............. 31
Cardiac Evaluation of a Child with Stridor ........................................................................................ 33
Cardiac Evaluation of a Child with Systemic Hypertension .............................................................. 34
Cardiomyopathy and Myocarditis..................................................................................................... 35
Inflammatory Cardiovascular Disease .............................................................................................. 36
Prevention and Management of Infective Endocarditis ................................................................... 37
Management of Critically Ill Children with Cardiovascular Compromise ......................................... 38
Introduction
The Post CSCST Fellowship in Paediatric Cardiology is a one year programme designed to dovetail
with the Higher Specialist Training programme in General Paediatrics. It takes into account the major
areas of competence required by the subspecialist in Paediatric Cardiology and will be supervised by
the Faculty of Paediatrics of the Royal College of Physicians in Ireland. Completion of this program will
ensure the knowledge and competencies in all areas of the curriculum, meeting international standards
for best practice and allowing candidates to practice as a subspecialist in Paediatric Cardiology
Applicants for the Post CSCST Fellowship in Paediatric Cardiology will have successfully completed
the RCPI Higher Specialist Training programme in General Paediatrics within two years of the start date
of the Post CSCST Fellowship programme.
Prior experience in Paediatric Cardiology during General Paediatrics training would be an advantage.
The curriculum takes into account the major areas of competence required by the subspecialist in
Paediatric Cardiology and will be supervised by the Faculty of Paediatrics of the Royal College of
Physicians in Ireland. Doctors who have successfully completed the RCPI Higher Specialist Training
programme in General Paediatrics and are within two years of completion will be deemed eligible to
apply for the Post CSCST Fellowship in Paediatric Cardiology Completion of this program will ensure
the knowledge and competencies in all areas of the curriculum, meeting international standards for
best practice and allowing candidates to practice as a subspecialist in Paediatric Cardiology
Training Programme
The training programme offered will provide opportunities to fulfil all the requirements of the curriculum
of training for Paediatric Cardiology in approved training hospitals. Each post within the programme will
have a named trainer/educational supervisor and the programme will be under the direction of the
Faculty of Paediatrics of the Royal College of Physicians in Ireland.
Trainee Numbers
It is expected that the Post CSCST Fellowship in Paediatric Cardiology will be awarded to one candidate
per year.
ePortfolio
The trainee will be required to keep their ePortfolio up to date and maintained throughout their
Fellowship training. The ePortfolio will be countersigned as appropriate by the Trainer to confirm the
satisfactory fulfilment of the required training experience and the acquisition of the competencies set
out in the Curriculum. This will remain the property of the Trainee and must be produced at the end
of year Evaluation meeting. At the end of year Evaluation, the ePortfolio will be examined. The results
of any assessments and reports by the named trainer/educational supervisor, together with other
material capable of confirming the trainee’s achievements, will be reviewed.
Programme Management
Coordination of the training programme will lie with the Medical Training Department.
The training year will usually run from July to July in line with HST programmes
Annual evaluations will usually take place between April and June each year
Each trainee will be registered to the ePortfolio and will be expected to fulfil all requirements
relating to the management of yearly training records
Opportunities for audit and research may be available
Each trainee will be issued with a training agreement on appointment to the training
programme and will be required to adhere to all policies and procedures relating to Post
CSCST Fellowships.
Specialty Section
Objective: To be able to recognise nutrition and growth problems related to congenital heart
disease and direct appropriate strategies to optimise nutritional intake and maximise growth
KNOWLEDGE
SKILLS
Understand the management of fluid intake and fluid balance around the time of cardiac
surgery
Recognise failure to thrive and be able to identify cardiac and non-cardiac causes
Identify iron deficiency in patients with cyanotic congenital heart disease
Recognise the complications of long term nasogastric feeding regimens and the role of
specialist speech and language therapists
Recognise the importance of nursing staff and dieticians in supervising and advising on
nutrition
Provide information to parents about feeding regimes
Institute and monitor feeding regimes in children with cardiac failure
Identify when failure to thrive has not responded to optimising nutrition and make timely
referral to specialist cardiac team for decision regarding potential surgical intervention in
congenital heart disease patients.
Appropriate referral to the dietetics department
Lifestyle
Objective: To know about, promote, and support lifestyle measures to minimise cardiovascular risk
KNOWLEDGE
The lifestyle risk factors for adverse outcome in patients with cardiac conditions including:
o diet
o exercise
o social deprivation
o occupation
The effect of obesity on health with particular relevance to cardiac conditions
The effects of smoking on health with particular relevance to cardiac conditions
The effects of illicit drugs and alcohol on health with particular relevance to cardiac
conditions
SKILLS
KNOWLEDGE
The range and significance of symptoms associated with congenital and acquired diseases of
the cardiovascular system in all ages
The physical signs that may be found on examination of the cardiovascular system and how
to interpret those findings
The characteristic clinical features of different congenital cardiac defects
The characteristic features of innocent murmurs
Understand the likely concerns of parents of children who have been referred for evaluation
of a heart murmur
Understand the limitations of echocardiography and the need to discuss cases with the
specialist cardiologist, when appropriate
SKILLS
DOPS: Echocardiography
Record of 400 echocardiograms (250 supervised)
MiniCex:
Identification Innocent murmur and normal
Indications for echocardiogram
KNOWLEDGE
SKILLS
The indications for an exercise test, ambulatory ECG, cardiac event recorder and tilt-table
test in the investigation of these conditions and know when these tests should be done
under the guidance of the specialist cardiac centre
The role of genetic testing in families with possible or proven inherited congenital cardiac
conditions
Take an appropriate detailed history, eliciting all information that may help discriminate
between cardiac and non-cardiac causes of chest pain, palpitations and syncope
Make a logical provisional diagnosis on the basis of history and physical examination
Identify features on the 12-lead ECG that suggest a substrate for an arrhythmia
Identify ECG evidence of ischaemic heart disease and ventricular hypertrophy
Use echocardiography to accurately identify normal cardiac structure and function and to
recognise and make a correct initial diagnosis of abnormality
Make an appropriate plan for further investigation and follow-up
Complete the assessment quickly in an outpatient setting
Diagnose normality
Institute and monitor appropriate treatment for arrhythmias and vasovagal syncope
Explain the plan for further investigation and the reasons for this line of investigation in
terms understandable to the patient and parents
Explain the likely diagnosis and its impact on lifestyle
Provide reassurance where there is no organic cause for symptoms
Refer appropriately to other specialties when a non-cardiac cause is likely
DOPS:
o 12 Lead ECG
o Exercise testing
o Echocardiography
Record of:
o 10 Exercise tests
o 400 Echocardiograms (250 supervised)
MiniCex
Arrhythmias
Objective: To be able to carry out assessment and treatment of children and adolescents with
arrhythmias in liaison with the specialist cardiac centre
KNOWLEDGE
The natural history, presentation and clinical features of common arrhythmias from foetus
to adolescent
Know the mechanisms involved in the development of cardiac arrhythmias
The genetic disorders associated with cardiac arrhythmias and indications for genetic
referral
The types of structural heart disease and types of cardiac surgery associated with
arrhythmias
The characteristic ECG findings of common tachyarrhythmias and bradyarrhythmias, and the
features suggesting risk of arrhythmia in the resting ECG
The indications for exercise testing, ambulatory monitoring, and external loop ECG recording
Understand the classification, mechanism of action, interactions, side effects,
contraindications and clinical use of antiarrhythmic drugs in paediatric patients
Know the indications for DC cardioversion and defibrillation
SKILLS
Take a history in a patient with palpitations, perform an expert examination and decide
whether an arrhythmia is likely
Form an appropriate plan of further investigation in a patient with suspected arrhythmias
Recognise and manage SVT from neonatal to adolescent life, in liaison with SSC or CCC
Identify the type of arrhythmia present from a 12 lead ECG capturing a rhythm abnormality
Interpret 24 hour and external loop ECG recordings, and know when to seek further help in
interpretation
Supervise an exercise test and make an initial interpretation of the results
Perform vagal manoeuvres, DC cardioversion, and defibrillation appropriately in the
emergency treatment of tachyarrhythmias
Explain the rationale, side effects and risks of arrhythmia treatments (including expectant
approach) to patients and their families
Explain the common arrhythmias and their associated risks to patients and their families
Offer appropriate management options and warning signs to the patient and family
Provide advice in respect of sports and exercise
Identify possible inherited cardiac conditions and refer to specialist centre and clinical
geneticist
Understand the importance of patient education in managing ongoing symptoms and
determining the most appropriate treatment for each individual
Know limitations and when to refer to a specialist paediatric cardiologist for expert advice,
assessment, and management of arrhythmias
Perform and interpret an ECG taken during an adenosine challenge
Select the appropriate emergency treatments and be familiar with the longer term drug
treatments used by the specialist unit for common tachyarrhythmias
DOPS:
o Vagal manoeuvres
o DC cardioversion
o Defibrillation
o ECG –adenosine challenge
ACLS or APLS
KNOWLEDGE
The physiology of duct dependent systemic and pulmonary circulation
The natural history, anatomy, physiology and clinical features of cardiac disorders that cause
collapse in infancy
The cardiac causes of cardiovascular collapse and likely diagnoses on the basis of the timing
of presentation
How to distinguish cardiac and non-cardiac causes of cardiovascular collapse
The indications, contraindications, and side effects of prostaglandin E therapy for duct
dependent systemic and pulmonary circulation
Know the impact of cardiovascular collapse on other organs
The indications, limitations and risks of non-invasive and invasive investigation of infants
that present with collapse
The ECG, CXR and echocardiographic findings in congenital heart disease presenting with
collapse in infancy
Understand the principles of angiographic and haemodynamic assessment with cardiac
catheterisation for infants who present with collapse and congenital heart disease
Know the role and risks of catheter intervention and surgery in congenital heart presenting
with collapse
SKILLS
Take a relevant history and perform an appropriate examination
Interpret ECG, CXR and blood results and appreciate their importance and limitations in
reaching a diagnosis
Initiate prostaglandin E where appropriate and know how to monitor its effect and when to
alter the dose administered prior to transfer to SSC
Recognise and respond appropriately to the urgency of the clinical situation
Identify cardiovascular collapse and carry out or direct resuscitation, medical treatment
including high dependency care, and stabilisation prior to transfer to SSC
Use echocardiography as an aid to recognising and/or making a provisional diagnosis of
abnormalities in cardiac structure or function associated with collapse in infancy
Understand the difficulties in diagnosing some cardiac abnormalities on echocardiography
and to liaise with the SSC or CCC as appropriate.
Identify where information is incomplete and refer appropriately for to SSC or CCC for
further investigation either by non-invasive imaging or cardiac catheterization
KNOWLEDGE
Physiology of cardiac failure caused by:
Pressure overload
Volume overload
Restriction to inflow
Reduced contractility
Physiology of pulmonary oedema
The natural history, anatomy, physiology and clinical features of disorders that cause cardiac
failure at different ages, from newborn to adult life
The causes of cardiac failure and identify likely diagnoses on the basis of the timing of
presentation
How to distinguish cardiac failure from other causes of increased respiratory effort
The indications, contraindications, action and side-effects of drug treatment for cardiac
failure
The ECG, CXR and key echocardiographic findings in cardiac disorders presenting with
cardiac failure
SKILLS
Identify cardiac failure in paediatric patients throughout childhood.
Take a relevant history and perform an appropriate examination
Make a provisional anatomical and physiological diagnosis of the cause of cardiac failure on
the basis of the clinical information and investigations, prior to referral to the specialist
centre
Optimise nutrition and manage failure to thrive caused by cardiac failure
Appreciate the role of cardiac nurses and cardiac community nurses in managing chronic
cardiac failure
Interpret ECG, CXR and blood results and appreciate the importance and limitations of these
investigations in diagnosing cardiac failure and elucidating its underlying cause
Use echocardiography to look for and/or provisionally diagnose abnormalities in cardiac
structure or function associated with cardiac failure in infants and children prior to timely
transfer to SSC or CCC.
Identify where information is incomplete and refer appropriately to a SSC or CCC for further
investigation either by non-invasive imaging or cardiac catheterisation
Institute appropriate drug therapy for cardiac failure and monitor its success and
complications
KNOWLEDGE
The principal anatomy, physiology, epidemiology, natural history, associations, and genetic
implications of the main acyanotic congenital heart defects including:
o Atrial septal defect
o Ventricular septal defect
o Atrioventricular septal defect
o Patent arterial duct
o Aortopulmonary septal defect
o Pulmonary stenosis
o Aortic stenosis
o Coarctation of the aorta
o Interrupted aortic arch
o Hypoplastic left heart syndrome
The impact of left to right shunts on pulmonary vascular resistance and the physiology of
Eisenmenger syndrome
The nature and timing of clinical presentations and long term complications of the above
acyanotic congenital heart defects
The key ECG, CXR and echocardiographic findings of the main lesions
The national recommendations regarding the prevention and management of infective
endocarditis
The indications, limitations and risks of non-invasive and invasive investigation
The principles of angiographic and haemodynamic assessment by cardiac catheterisation
The range of surgical and catheter intervention treatment options including their main
advantages and success rates, disadvantages and complications
The normal course of postoperative recovery and potential complications after surgery for
the main lesions
SKILLS
Make a provisional diagnosis and discriminate between acyanotic defects on the basis of
presentation, clinical findings, ECG and CXR
Use transthoracic echocardiography to make a provisional diagnosis of acyanotic defects and
to define their main anatomical and physiological characteristics
KNOWLEDGE
The physiology of cyanosis caused by:
o Right heart obstruction with right to left shunting
o Parallel circulation
o Common mixing lesions
Understand the physiology of duct dependent pulmonary circulation
The natural history, anatomy, physiology and clinical features of congenital heart disease
causing cyanosis in the newborn period
How to distinguish cardiac and non-cardiac causes of cyanosis in the newborn period
The indications, limitations and risks non-invasive and invasive investigation in newborns
The ECG, CXR and echocardiographic findings for the main cyanotic lesions presenting in
infancy
The indications, contraindications, and side effects of prostaglandin E therapy for duct
dependent pulmonary circulation
The role and risks of catheter intervention and surgery in congenital heart disease
presenting with cyanosis in the newborn period
Understand the principles of angiographic and haemodynamic assessment by cardiac
catheterisation for neonates who present with cyanosis and congenital heart disease
SKILLS
DOPS
Echo
Record of 400 echocardiograms (250 supervised)
KNOWLEDGE
The principal anatomy, physiology, epidemiology, natural history, associations and genetic
implications of the main cyanotic congenital heart defects including:
o Pulmonary atresia with intact ventricular septum
o Pulmonary atresia with ventricular septal defect
o Critical pulmonary stenosis
o Tetralogy of Fallot
o Absent pulmonary valve syndrome
o Transposition of the great arteries with intact ventricular septum
o Transposition of the great arteries with ventricular septal defect
o Double outlet right ventricle
o Common arterial trunk
o Total anomalous pulmonary venous connection
o Univentricular atrioventricular connection
o Complex congenital heart disease associated with abnormalities of cardiac position
and situs
Know the nature and timing of clinical presentations and long term complications of the
above
The indications, limitations and risks of non-invasive and invasive investigation
Understand the principles of angiographic and haemodynamic assessment by cardiac
catheterisation for patients with cyanotic congenital heart disease
Know the normal course of postoperative recovery after surgery for each type of cyanotic
cardiac defect
The ECG, CXR and echocardiographic findings in patients with cyanotic congenital heart
disease
The range of surgical and catheter intervention treatment options for cyanotic cardiac
defects including their main advantages and success rates, disadvantages and complications
SKILLS
Make a provisional diagnosis and discriminate between the various cyanotic defects on the
basis of presentation, clinical findings, ECG and CXR
Provide first line emergency treatment for cyanotic spells and liaise with the specialist centre
about further management
Identify when there is cyanosis combined with cardiac failure and initiate medical treatment
when necessary
Appreciate the concerns and anxiety of parents and other family members
Liaise with the SSC or CCC for advice and/or evaluation when necessary
Communicate effectively with the with SSC or CCC for the joint management of patients
DOPS
o Transthoracic echography
Record of 400 echocardiograms (250 supervised)
Objective: To be able to carry out and interpret the 12 lead ECG throughout childhood
KNOWLEDGE
The principles of electrophysiology relating to the production of the ECG and limitations of
the ECG and of differing ECG machines
The standard lead placement for paediatric ECG recording and lead placement for
dextrocardia
Age related changes in ECG wave forms
How to evaluate rhythm, hypertrophy, ischaemia, injury and infarction on ECG
The features of ECG produced using epicardial pacing wires
SKILLS
Perform a 12 lead ECG with accurate lead placement appropriate to the age of the child
Interpret ECG in relation to age related changes
Recognise and interpret abnormal QRS axis, atrial enlargement, normal and abnormal
patterns of atrial depolarisation, ventricular hypertrophy, normal and abnormal patterns of
ventricular depolarisation, normal and abnormal ventricular repolarisation, bundle branch
block, heart block, pre-excitation and tachyarrhythmias on the ECG
DOPS
o Perform and interpret ECG
Mini Cex
Record 300 ECGs
Chest X-Ray
Objective: To be able to interpret a CXR to assist diagnosis and assessment of cardiac conditions
throughout childhood
KNOWLEDGE
SKILLS
Diagnose abnormalities in cardiac position and identify when great artery arrangement is
abnormal on CXR
Interpret patterns of pulmonary vasculature on CXR
Recognise lung pathology on CXR
Use information on the CXR to assist in making an anatomical and physiological diagnosis in
congenital heart disease
DOPS
o CXR
o Interpret 40 CXR
Transthoracic Echocardiography
Objective: To be able to perform transthoracic echocardiography throughout childhood to diagnose
and assess the common forms of congenital and acquired heart disease and recognise where further
more expert assessment is essential
It is recognised that achieving these objectives to a full level of competence will not occur during a
single year. It is essential that this competency is formally assessed during training across the range
of structural and functional heart conditions. (Standards for this assessment are detailed in Appendix
1, Section 4.3). Focused continued professional development will be required and formal accreditation
is strongly recommended. Currently, the only individual certification pathway and revalidation
pathway is via the European route under the auspices of the European Association of
Echocardiography and endorsed by the Association of European paediatric cardiology (AEPC) and
European society of cardiology (ESC). Ongoing regular personal audit and peer review of practice
throughout the doctor's career will be necessary. It is essential that an awareness of personal
limitations and confidence to seek review of findings is maintained and that the implications of a
failure to recognise important abnormality are appreciated.
KNOWLEDGE
SKILLS
Perform echocardiography to assist the specialist cardiologist during visiting clinics
Schedule cases for review and audit of echocardiographic assessment
Develop and work within guidance regarding the range of appropriate cases agreed with the
specialist centre
Interpret the significance and reliability of the information obtained by echocardiography
Demonstrate ability to work with and share expertise mutually with echocardiography
technicians
DOPS
o Echocardiograpy
ECHO Course (EAE course)
EAE Certification exam
Record of 400 echocardiograms (250 supervised)
KNOWLEDGE
The indications for an ambulatory ECG and external cardiac loop recorder
The normal range of findings on a paediatric 24 hour ECG
Understand the limitations of these non-invasive ECG investigations
SKILLS
Scan the results of these investigations select appropriate highlights and produce an
accurate report
Interpret the results in the clinical context
DOPS
o Interpret and perform ambulatory ECG
Record 300 number of ambulatory ECGs
KNOWLEDGE
SKILLS
DOPS
o Interpret ambulatory blood pressure monitoring
Exercise Tests
Objective: To be able to carry out and interpret exercise tests appropriately in the diagnosis and
assessment of children with cardiac conditions
KNOWLEDGE
SKILLS
DOPS
o Perform and interpret exercise tests
Record 10 exercise tests
KNOWLEDGE
Know the indications for and possible interpretations of adenosine challenges during
tachycardias
SKILLS
DOPS
o Perform adenosine challenge ECG
Record 5 adenosine challenge ECGs
KNOWLEDGE
SKILLS
Refer for tilt table testing appropriately and with a clear objective
Make an initial interpretation of the findings of a tilt table test
DOPS
DOPS
o DC cardioversion
Record of 1 DC cardioversion
ACLS/APLS
Cardiac Pacing
Objective: To understand the principles of temporary and permanent pacing and pacemaker
monitoring
KNOWLEDGE
SKILLS
Be able to recognize appropriate and non-functioning pacing on the surface ECG
ECG Course
DOPS
o Interpret non-functioning pacing on ECG
Attend 3 pacing clinics
KNOWLEDGE
Know the main cardiac abnormalities found in common genetic disorders and syndromes
including:
o Trisomy 21 (Down syndrome)
o Trisomy 18 (Edwards Syndrome)
o Trisomy 13 (Patau syndrome)
o Monosomy XO (Turner syndrome)
o Noonan syndrome
o Williams syndrome
o Alagille syndrome
o Marfan syndrome
o 22q11 deletion
o CHARGE association
o VACTERL association
o Inherited arrhythmias including channelopathies
SKILLS
Be aware of the main cardiac abnormalities found in less common genetic disorders and
syndromes including:
o Storage diseases
o Neuromuscular diseases
o Mitochondrial cytopathies
o Hyperlipidaemias
o Inherited Cardiomyopathies
Know the prognosis of genetic syndromes and their associated cardiac disorders
Understand the importance and practice of screening for cardiac conditions with a genetic
basis
Be aware of the importance of fetal cardiology review for future pregnancies
Recognise the importance of the multidisciplinary team in the management of patients in
this group
Recognise the impact of other features of the genetic disorder or syndrome on cardiac
management
Be willing to discuss the possibility of recurrence of the cardiac disorder in subsequent
children whilst recognising the role of the clinical geneticist in expert counselling of parents
about recurrence
Use transthoracic echocardiography to screen, recognise and/or diagnose specific
abnormalities in cardiac structure or function related to genetic disorders and syndromes
DOPS
o Transthoracic echography
Record of 250 Transthoracic echocardiography
Objective: To be able to carry out preliminary specialist cardiac assessment of children with stridor
and know when it is appropriate to refer to the specialist cardiac centre for further evaluation or
treatment
KNOWLEDGE
The embryology, anatomy and natural history of vascular rings and slings and their
association with additional lung pathology
How to distinguish the cardiac and non-cardiac causes of stridor throughout childhood
The limitations of transthoracic echocardiography in the identification of vascular rings
The role and features of vascular rings and slings on CXR, barium swallow, and bronchoscopy
The role and key features of vascular rings and slings on angiography and MRI
The role of surgery and main surgical options for release of rings and slings
Understand the transthoracic echocardiographic findings specific to vascular rings and slings
SKILLS
Discuss the main causes, natural history and management of stridor with parents, offering
reassurance or referral to the specialist centre as appropriate
Be aware of the role of thoracic surgeons in children with associated lung abnormalities
Undertake initial transthoracic echocardiography with the aim of positively identifying the
presence of vascular rings and slings to aid discussion and planning with specialist centre
Select patients who merit referral to specialist cardiac centre for further investigation by
advanced echocardiography, bronchoscopy, CT, angiography or MRI
MiniCex
KNOWLEDGE
SKILLS
MiniCex
KNOWLEDGE
The causes, physiology, pathology, natural history, prognosis and clinical features of
myocarditis
The role of genetics in cases of cardiomyopathy and importance of working with the clinical
geneticist/inherited cardiovascular disease service
The range of medical and surgical treatments available for patients with cardiomyopathy
and indications for referral
Be aware of the available forms of circulatory support (LVAD, ECMO)
Be aware of the role of cardiac transplantation in end-stage cardiomyopathy
SKILLS
Be familiar with the main causes, physiology, pathology, natural history, prognosis, genetic
implications and clinical features of dilated, hypertrophic and restrictive cardiomyopathy
Recognise features in the history and examination of myocarditis or cardiomyopathy
Initiate management of cardiac failure and low cardiac output caused by myocarditis or
cardiomyopathy and liaise appropriately with the specialist cardiac centre regarding further
management
Involve the genetics team where appropriate
Show sensitivity in counselling parents with a child severely affected by cardiomyopathy
Involve parents in decision making in planning management for end-stage cardiomyopathy
in consultation with the SSC or CCC.
Carry out an initial diagnostic transthoracic echocardiographic evaluation of a child with
myocarditis or cardiomyopathy including assessment of cardiac function for discussion with
specialist centre
Exclude conditions which may mimic cardiomyopathy including coronary artery assessment
Recognise the likely prognosis given by the specialist centre and be able to discuss this with
the family if required
Consider other aspects of disorders underlying the cardiomyopathy or other organs affected
in planning for treatment in end-stage cardiomyopathy
MiniCex
Study Day
The pathology and natural history of rheumatic fever, Kawasaki disease and collagen
vascular disease affecting the cardiovascular system
The cardiac and non-cardiac manifestations of these disorders
The anatomical and echocardiographic features of these disorders
The current recommendations for investigation and treatment of acute and chronic
Kawasaki disease
The current recommended drug therapy for acute rheumatic fever and the long term
sequelae
Understand the importance of primary and secondary prevention in rheumatic fever
SKILLS
Recognise the clinical features of Kawasaki disease and carry out transthoracic
echocardiographic examination of the coronary arteries, maintaining an awareness of the
difficulties of such assessment and the importance of specialist centre opinion
Initiate acute management for Kawasaki disease, and liaise with the specialist cardiac centre
regarding the long-term management and appropriate follow up programme.
Be able to identify the features suggesting rheumatic heart disease on transthoracic
echocardiography prior to mandatory referral of such cases for specialist centre assessment
Initiate the acute treatment for rheumatic fever and recognise the indications for referral to
the specialist cardiac centre for intervention or surgery in patients with rheumatic heart
disease
Cooperate with other specialties in the investigation of collagen vascular diseases with
cardiovascular involvement
Understand the indications for referral for specialist investigation including coronary
angiography in children with Kawasaki disease
MiniCex
KNOWLEDGE
SKILLS
Objective: To be able to make an assessment and initiate treatment of children who are critically ill
with severe haemodynamic disturbance
KNOWLEDGE
SKILLS
Recognise the clinical signs of low cardiac output and the clinical signs of progression to
shock
Recognise the biochemical markers of low cardiac output
Use fluid management and inotropic support appropriately to optimise cardiac output and
tissue oxygen delivery
Recognise the need for intensive care support for children with haemodynamic instability
and liaise with intensive care colleagues and specialist units as appropriate
Communicate the findings of the cardiac assessment clearly and logically with colleagues
Use transthoracic echocardiography to assist in determining the cause of haemodynamic
instability
KNOWLEDGE
SKILLS
Identify probable congenital heart disease in premature and low birth weight infants and
make an initial management plan, including the likely and most appropriate timing of
transfer to specialist cardiac centre
KNOWLEDGE
The indications for and timing of active and passive immunisation for children with cardiac
conditions (and their families where applicable) in addition to the routine immunisation
schedule
Indications for prophylactic measures to minimise severe illness following infective
exposures
The implications of primary and secondary immunodeficiency associated with cardiac
conditions or their treatment, and the potential impact on transfusion, immunisation, and
other prevention strategies
SKILLS
Recognise which patients should receive additional immunisation and refer or organise this
appropriately
Screen for primary immune deficiency and refer patients for immunology assessment and
advice when appropriate
Advise patients, parents and other health professionals about the therapeutic and lifestyle
implications and risks of primary and secondary immune dysfunction
Offer sound advice to patients and their families regarding the secondary effect of cardiac
therapies on immunity and immunisation
Pulmonary Hypertension
Objective: To make a provisional diagnosis of pulmonary hypertension, be involved in shared care
follow up with the specialist cardiac centre, and understand the key management issues for patients
KNOWLEDGE
SKILLS
Perform a complete history and physical examination to recognise the presence or evolution
of pulmonary hypertension
KNOWLEDGE
The cardiac disorders associated with high risk during general anaesthesia (for which surgery
and any preoperative assessment should be carried out in specialist cardiac centre)
The role and limitations of play specialists and psychologists in preparing children for surgery
SKILLS
Identify patients who are at increased risk from anaesthesia and recommend when
appropriate for anaesthetic to be carried out in setting of SSC/CCC as appropriate
Select patients who require further investigation by ECG, CXR or echocardiography
Answer questions from patients and their parents about the impact of their cardiac
condition on the safety of anaesthesia and surgery
Obtain information which would allow determination of the physiology of the cardiac
abnormality and make an assessment of the potential cardiac considerations for anaesthetic
using ECG,
CXR and echocardiography, and seek full discussion with SCC/CCC regarding any conclusions
Liaise with the anaesthetist and surgeon with clear advice about the relevance of any cardiac
condition and ensure that the specialist paediatric cardiologist's advice has been sought
prior to consideration of any surgery or anaesthetic in high risk cases
Liaise with specialist cardiologists to recommend an appropriate fluid regime and how
cardiac drugs are to be administered in the perioperative period
Minimum Form
Curriculum Requirement Required/Desirable Requirement Reporting Period Name
Section 1 - Training Plan
Training Programme
Weekly Timetable (Sample Weekly Timetable for Post/Clinical Attachment) Required 1 Form 045
Personal Goals Plan (Copy of agreed Training Plan for your current training year signed by both Training Programme
Trainee & Trainer) Required 1 Form 052
Training Programme
Personal Goals Review Form Desirable 1 Form 137
Training Programme
On Call Rota Required 1 Form 064
Section 2 - Training Activities
Outpatient Clinics
Training Programme
General paediatric clinics Required 80 Form 001
Training Programme
Pacing Clinics Required 3 Form 001
Training Programme
Pulmonary hypertension Required 2 Form 001
Ward Rounds/Consultations
Training Programme
Consultant Led (minimum 1 per week) Required 40 Form 002
Minimum Form
Curriculum Requirement Required/Desirable Requirement Reporting Period Name
Training Programme
Consultations Required 40 Form 002
Emergencies/Complicated Cases Desirable 1 Training Programme Form 003
Procedures/Practical Skills/Surgical Skills
Echocardiography (250 supervised) Required 400 Training Programme Form 004
Transthoracic echo Required 250 Training Programme Form 004
Exercise testing Required 10 Training Programme Form 004
Interpret ECG (250 supervised) Required 300 Training Programme Form 004
Interpret CXR Required 40 Training Programme Form 004
Adenosine challenge ECG Required 5 Training Programme Form 004
Tilt table testing Required 10 Training Programme Form 004
DC cardioversion Required 1 Training Programme Form 004
Immunization for immune deficient asplenic/22q11 patients Required 5 Training Programme Form 004
Additional/Special Experience Gained Desirable 1 Training Programme Form 005
Relatively Unusual Cases Desirable 1 Training Programme Form 019
Chronic Cases/Long term care Desirable 1 Training Programme Form 066
ICU/CCU Cases Desirable 1 Training Programme Form 090
Management Experience Desirable 1 Training Programme Form 110
Section 3 - Educational Activities
Mandatory Courses
ACLS/APLS Required 1 Training Programme Form 006
ECHO course (EAE) Required 1 Training Programme Form 006
ECG course Required 1 Training Programme Form 006
Non – Mandatory Courses Desirable 1 Training Programme Form 007
Training Programme
Study Days (assist in conducting cardiology or echocardiography study days) Required 3 Form 008
Training Programme
National/International meetings (PECSIG, BCCA or AEPC) Required 1 Form 010
In-house activities
Minimum Form
Curriculum Requirement Required/Desirable Requirement Reporting Period Name
Training Programme
Grand Rounds (minimum of 1 per month) Required 10 Form 011
Training Programme
Cardiology Meeting (average 1 per week) Required 40 Form 011
Training Programme
Other (minimum of 1 per month from the categories below: )
Training Programme
Journal Club Required 2 Form 011
Training Programme
Radiology Conferences Required 2 Form 011
Training Programme
Pathology Conferences Required 2 Form 011
Training Programme
MDT Meetings Required 2 Form 011
Training Programme
Seminar Required 2 Form 011
Training Programme
Lecture Required 1 Form 013
Examinations
EAE certification Required 1 Training Programme Form 012
Formal Teaching Activity minimum 1 formal teaching session per month from the categories
below:
Lecture
Tutorial
Bed side Teaching
Required 10 Training Programme Form 013
Research Activities Desirable 1 Training Programme Form 014
Training Programme
Audit or Quality improvement activities Required 1 Form 015
Training Programme
Clinical Audit Report form Required 1 Form 135
Training Programme
Publications Desirable 1 Form 016
Minimum Form
Curriculum Requirement Required/Desirable Requirement Reporting Period Name
Training Programme
Presentations Required 1 Form 017
Training Programme
National/International meetings (minimum 1 per year) Required 1 Form 010
Committee Attendance Desirable 1 Training Programme Form 063
Additional Qualifications Desirable 1 Training Programme Form 065
Section 4 - Assessments
CBD Required 1 Year of Training Form 020
DOPS
Fluid and electrolyte balance Required 1 Training Programme Form 021
Echocardiography Required 1 Training Programme Form 021
Transthoracic echography Required 1 Training Programme Form 021
12 Lead ECG – perform and interpret Required 1 Training Programme Form 021
Exercise Testing Required 1 Training Programme Form 021
ECG – adenosine challenge Required 1 Training Programme Form 021
Vagal maneuvers Required 1 Training Programme Form 021
DC cardioversion Required 1 Training Programme Form 021
Defibrillation Required 1 Training Programme Form 021
Interpret CXR Required 1 Training Programme Form 021
Interpret ambulatory blood pressure monitoring Required 1 Training Programme Form 021
Adenosine challenge ECG Required 1 Training Programme Form 021
Tilt table testing Required 1 Training Programme Form 021
DC cardioversion Required 1 Training Programme Form 021
Interpret non functioning pacing on ECG Required 1 Training Programme Form 021
Mini-CEX (At least two Mini-CEX assessments) Required 2 Year of Training Form 023
Quarterly Assessments Required 4 Year of Training Form 092
End-of-Post/End-of-Year Assessments Required 1 Year of Training Form 092