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Mitochondrial tRNA 3' end metabolism and human disease.
scientific article published on 11 October 2004
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524294
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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15477393%20AND%20SRC:MED&resulttype=core&format=json
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4 January 2020
review article
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title
Mitochondrial tRNA 3' end metabolism and human disease
(English)
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Europe PubMed Central
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524294
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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15477393%20AND%20SRC:MED&resulttype=core&format=json
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4 January 2020
author
Mario Mörl
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2
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524294
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4 January 2020
author name string
Louis Levinger
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1
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524294
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4 January 2020
Catherine Florentz
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3
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524294
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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15477393%20AND%20SRC:MED&resulttype=core&format=json
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English
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publication date
11 October 2004
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524294
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4 January 2020
published in
Nucleic Acids Research
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Europe PubMed Central
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524294
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4 January 2020
volume
32
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524294
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4 January 2020
issue
18
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4 January 2020
page(s)
5430-5441
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Europe PubMed Central
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4 January 2020
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Mitochondrial diseases in man and mouse
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Mitochondrial DNA mutations and pathogenesis
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11 July 2018
Molecular phenotype of a human lymphoblastoid cell-line homoplasmic for the np 7445 deafness-associated mitochondrial mutation.
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11 July 2018
Distribution of both lengths and 5' terminal nucleotides of mammalian pre-tRNA 3' trailers reflects properties of 3' processing endoribonuclease
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11 July 2018
Molecular genetic aspects of human mitochondrial disorders
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11 July 2018
The importance of being modified: roles of modified nucleosides and Mg2+ in RNA structure and function.
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11 July 2018
Human mitochondrial tRNA processing
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11 July 2018
C to U editing and modifications during the maturation of the mitochondrial tRNA(Asp) in marsupials
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11 July 2018
tRNA punctuation model of RNA processing in human mitochondria
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11 July 2018
Distinctive features of the 5'-terminal sequences of the human mitochondrial mRNAs
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PubMed Central
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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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11 July 2018
Sequence and organization of the human mitochondrial genome
1 reference
stated in
PubMed Central
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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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11 July 2018
URF6, last unidentified reading frame of human mtDNA, codes for an NADH dehydrogenase subunit
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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11 July 2018
Kearns-Sayre syndrome with muscle mitochondrial DNA deletion
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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11 July 2018
Human cells lacking mtDNA: repopulation with exogenous mitochondria by complementation
1 reference
stated in
PubMed Central
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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
retrieved
11 July 2018
Recognition of tRNA by the enzyme ATP/CTP:tRNA nucleotidyltransferase. Interference by nucleotides modified with diethyl pyrocarbonate or hydrazine
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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11 July 2018
Characterization of an RNase P activity from HeLa cell mitochondria. Comparison with the cytosol RNase P activity
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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11 July 2018
Unilateral aminoacylation specificity between bovine mitochondria and eubacteria
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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11 July 2018
Defects in mitochondrial protein synthesis and respiratory chain activity segregate with the tRNA(Leu(UUR)) mutation associated with mitochondrial myopathy, encephalopathy, lactic acidosis, and strokelike episodes
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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11 July 2018
Cytidines in tRNAs that are required intact by ATP/CTP:tRNA nucleotidyltransferases fromEscherichia coliandSaccharomyces cerevisiae
1 reference
stated in
PubMed Central
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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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11 July 2018
Exchange of regions between bacterial poly(A) polymerase and the CCA-adding enzyme generates altered specificities
1 reference
stated in
PubMed Central
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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
A pathogenesis-associated mutation in human mitochondrial tRNALeu(UUR) leads to reduced 3'-end processing and CCA addition.
1 reference
stated in
PubMed Central
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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
The pathogenic A4269G mutation in human mitochondrial tRNA(Ile) alters the T-stem structure and decreases the binding affinity for elongation factor Tu.
1 reference
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PubMed Central
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24 September 2018
The Caenorhabditis elegans homolog of the putative prostate cancer susceptibility gene ELAC2, hoe-1, plays a role in germline proliferation
1 reference
stated in
PubMed Central
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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
Interdomain communication between weak structural elements within a disease-related human tRNA.
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
Towards understanding human mitochondrial leucine aminoacylation identity.
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PubMed Central
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24 September 2018
Decreased CCA-addition in human mitochondrial tRNAs bearing a pathogenic A4317G or A10044G mutation
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
Dimerization of a pathogenic human mitochondrial tRNA.
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
The 7472insC mitochondrial DNA mutation impairs the synthesis and extent of aminoacylation of tRNASer(UCN) but not its structure or rate of turnover
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
Charging levels of four tRNA species in Escherichia coli Rel(+) and Rel(-) strains during amino acid starvation: a simple model for the effect of ppGpp on translational accuracy.
1 reference
stated in
PubMed Central
reference URL
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24 September 2018
Fragile T-stem in disease-associated human mitochondrial tRNA sensitizes structure to local and distant mutations
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
Functional defects of pathogenic human mitochondrial tRNAs related to structural fragility
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stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
retrieved
24 September 2018
A Watson-Crick base-pair-disrupting methyl group (m1A9) is sufficient for cloverleaf folding of human mitochondrial tRNALys.
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
MtDNA mutation in MERRF syndrome causes defective aminoacylation of tRNA(Lys) and premature translation termination
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
Separation and characterization of 5'- and 3'-tRNA processing nucleases from rat liver mitochondria.
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PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=524294
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24 September 2018
Impairment of tRNA processing by point mutations in mitochondrial tRNA(Leu)(UUR) associated with mitochondrial diseases
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PubMed
reference URL
https://pubmed.ncbi.nlm.nih.gov/15477393
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12 December 2020
based on heuristic
inferred from PubMed ID database lookup
Recombinant RNase Z Does Not Recognize CCA as Part of the tRNA and Its Cleavage Efficieny Is Influenced by Acceptor Stem Length
1 reference
stated in
PubMed
reference URL
https://pubmed.ncbi.nlm.nih.gov/15477393
retrieved
12 December 2020
based on heuristic
inferred from PubMed ID database lookup
Deletions of muscle mitochondrial DNA in patients with mitochondrial myopathies
1 reference
stated in
PubMed
reference URL
https://pubmed.ncbi.nlm.nih.gov/15477393
retrieved
12 December 2020
based on heuristic
inferred from PubMed ID database lookup
Purines in tRNAs required for recognition by ATP/CTP:tRNA nucleotidyltransferase from rabbit liver
1 reference
stated in
PubMed
reference URL
https://pubmed.ncbi.nlm.nih.gov/15477393
retrieved
12 December 2020
based on heuristic
inferred from PubMed ID database lookup
Abnormal RNA processing associated with a novel tRNA mutation in mitochondrial DNA. A potential disease mechanism
1 reference
stated in
PubMed
reference URL
https://pubmed.ncbi.nlm.nih.gov/15477393
retrieved
12 December 2020
based on heuristic
inferred from PubMed ID database lookup
Termination of quiescence in crustacea. The role of transfer RNA aminoacylation in the brine shrimp Artemia
1 reference
stated in
PubMed
reference URL
https://pubmed.ncbi.nlm.nih.gov/15477393
retrieved
12 December 2020
based on heuristic
inferred from PubMed ID database lookup
Identifiers
DOI
10.1093/NAR/GKH884
1 reference
stated in
Europe PubMed Central
PMC publication ID
524294
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15477393%20AND%20SRC:MED&resulttype=core&format=json
retrieved
4 January 2020
PMC publication ID
524294
1 reference
stated in
Europe PubMed Central
PMC publication ID
524294
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15477393%20AND%20SRC:MED&resulttype=core&format=json
retrieved
4 January 2020
PubMed publication ID
15477393
1 reference
stated in
Europe PubMed Central
PMC publication ID
524294
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15477393%20AND%20SRC:MED&resulttype=core&format=json
retrieved
4 January 2020
ResearchGate publication ID
8239391
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